Case Report - Scleromyxedema : An Atypical Form in a 50 Years Old Male Patient

Scleromyxedema is a chronic, progressive condition characterised by dermal fibrosis and mucinosis. The clinical variants consist of generalised confluent lichenoid eruptions (scleromyxedema) with systemic manifestations and a localised variant with discrete papular eruptions. The cases which do not fit into either of the category are termed as atypical or intermediate form. We report such a case of a 50 years old male patient with numerous asymptomatic erythematous papules mainly over his face and diffuse hyperpigmentation with thickening of skin of his body with no systemic complaints. All of his investigations were within normal limits and histopathology showed large amount of mucin deposit in reticular dermis with increased fibrocytes and increased spaces between collagen fibres.